Total Anomalous Pulmonary Venous Return

Description of various clips of TAPVR

Total anomalous pulmonary venous return (TAPVR) is a condition where the pulmonary veins will connect to the right atrium, instead of the left atrium. As such, there is an obligatory right to left shunting. The pulmonary venous return may become obstructed in the post-natal life, which is a neonatal emergency. TAPVR has variants, depending on where the pulmonary veins are draining into. Read more on TAPVR here.

Crab view with the abnormal connection of the pulmonary veins.

Altered course of the pulmonary veins seen here on parasternal long axis.

TAPVR draining to coronary sinus.

Case 1: Intracardiac location of TAPVR to coronary sinus non-obstructed

  • Intracardiac location of totally anomalous pulmonary venous connection to coronary sinus non-obstructed.

  • Large secundum atrial septal defect (ASD) shunting right to left.

  • Moderate to severe right ventricular dilation.

  • Underfilled left ventricle.

  • Straight ventricular septum in systole (right ventricular pressure overload).

  • Large nonrestrictive patent arterial duct (PDA) measuring 0.45 cm shunting bidirectionally.

Case 2: Supracardiac location of TAPVR to left-sided vertical vein non-obstructed

  • Supracardiac location of totally anomalous pulmonary venous connection(s) to left-sided vertical vein non-obstructed.

  • Moderate unrestrictive secundum atrial septal defect (ASD) within oval fossa shunting right to left.

  • Severe right ventricular dilation with straight ventricular septum.

  • Small anterosuperior trabecular muscular ventricular septal defect (VSD) shunting right to left.

  • Small restrictive patent arterial duct (PDA) shunting left to right

Created by Gabriel Altit - Neonatologist / Créé par Gabriel Altit (néonatalogiste) - © NeoCardioLab - 2020-2021 - Contact us / Contactez-nous